Low-grade malignant fibrous histiocytoma

Ai
Authors:
Low-grade-malignant-fibrous-histiocytoma-A-Axi-T1WI.jpg

A

Low-grade-malignant-fibrous-histiocytoma-B-Axi-T2WI.jpg

B

Low-grade-malignant-fibrous-histiocytoma-C-Cor-T1WI+C.jpg

C

Low-grade-malignant-fibrous-histiocytoma-D-Sag-T1WI+Csm.jpg

D

Clinical History: 
This 9-year-old boy presented with vision loss in the left eye for more than one year. Ophthalmologic exam revealed no organic lesion and the patient was referred for an MRI. The lesion was subsequently resected.

Diagnosis:
Low-grade malignant fibrous histiocytoma

MR Technique: 
Scans were acquired on a 1.5 T MR unit, using a 8-channel head coil. (A) Axial pre-contrast spin echo T1-weighted (TR/TE 375/14.2ms, 320×192 matrix) and (B) fast spin echo T2-weighted (TR/TE 3800/90ms) scans are displayed, in addition to (C) coronal and (D) sagittal post-contrast spin echo fat-suppressed T1-weighted scans. The slice thickness was 5 mm in each instance.

Imaging Findings:
A soft tissue mass is seen at the skull base, anteriorly, with a thin rim of low signal intensity, which on the corresponding CT exam (not shown) was noted to correspond to sclerotic bone. The lesion has a smooth border and is well demarcated, and compresses and displaces the left optic nerve. There is prominent homogeneous enhancement of the lesion.