Ollier Disease



Clinical History: 
This 17-year-old girl initially presented as a toddler and has since suffered from multiple complications related to Ollier disease, particularly in regard to her left femur. Disease involvement initially also included the left hemipelvis. The patient subsequently underwent multiple procedures involving the femur for the correction of pathologic fractures and leg-length discrepancies. Her most recent surgery, one year ago, consisted of curettage and bone grafting of lesions in her left iliac wing and proximal femur.

Ollier disease

MR Technique: 
Scans were acquired on a 1.5 T Siemens Espree MR unit. (A, B) Coronal spin echo T1-weighted (TR/TE 732/11 ms, scan time 2:11 min:sec) images and (C) Coronal turbo spin echo fat-suppressed T2-weighted (TR/TE 5190/67 ms, scan time 2:10 min:sec) images were obtained. Slice thickness was 6 mm in each instance.

Imaging Findings:
Innumerable chondroid lesions are identified within the left femoral metaphysis and more distal regions of the femur. These lesions exhibit ill-defined sclerosis and an expansile appearance on plain film radiography. Endosteal scalloping with thinning of the cortex, particularly along the anterolateral aspect the distal femur, is present. Similar lesions are identified within the patella and a few small lesions are seen within the proximal left tibial metaphysis.